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Description
moderate quality evidence) (Jamilian et al., 2017)

In diseases where amino-acid metabolizing enzymes are dysfunctional or absent (e.g., propionic acidemia and methylmalonic acidemias characterized by neurological symptoms, muscle weakness and low energy) C3 accumulates, and higher blood levels are used as a screening tool

L-carnitine can be effective when used at the right time

Wei P, He M, Wang Y, Han G

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